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GRANULOMATOUS SLACK SKIN: HISTOPATHOLOGY DIAGNOSIS PRECEDING CLINICAL MANIFESTATIONS BY 12 YEARS
Diagnosis
Granulomatous cutis laxa
Granulomatous slack skin
Lymphoma
Mycosis fungoides
Orcein staining
Treatment
Author
Affilliation
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Pathology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Pathology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. Hospital Universitário Clementino Fraga Filho. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Abstract
Background: Granulomatous slack skin is a very rare subtype of T-cell cutaneous lymphoma, characterized by the slow development of cutaneous sagging, especially on flexural areas. Its behavior is indolent and the treatment, in the majority of cases, disappointing. Main observations: We report a 54-year-old black patient with granulomatous slack skin, who at the beginning of the investigation showed intense xeroderma and generalized lymph node enlargement. The diagnosis was established based on histopathologic findings long before the disease’s characteristic clinical presentation appeared. Conclusion: During the twelve years of follow-up, the clinical manifestation evolved to marked skin looseness, most predominant in flexural regions, illustrating the clinical hallmark of granulomatous slack skin, long after first histological abnormalities were observed.
Keywords
Cutaneous T-cell lymphomaDiagnosis
Granulomatous cutis laxa
Granulomatous slack skin
Lymphoma
Mycosis fungoides
Orcein staining
Treatment
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