Author | Marinho, Flauberto Sousa | |
Author | Pirmez, Rodrigo | |
Author | Nogueira, Renata | |
Author | Cuzzi, Tullia | |
Author | Sodré, Celso Tavares | |
Author | Silva, Marcia | |
Access date | 2019-08-15T12:28:54Z | |
Available date | 2019-08-15T12:28:54Z | |
Document date | 2015 | |
Citation | MARINHO, Flauberto Sousa et al. Cutaneous manifestations in POEMS syndrome: case report and review. Case Reports in Dermatology, v. 7, p. 61-69, 2015. | pt_BR |
URI | https://www.arca.fiocruz.br/handle/icict/34833 | |
Description | Tullia Cuzzi. Fundação Oswaldo Cruz. Instituto Nacional de Infectologia Evandro Chagas. Documento produzido em parceria ou por autor vinculado à Fiocruz, mas não consta a informação no documento. | pt_BR |
Language | eng | pt_BR |
Publisher | Karger Publishers Open Access | pt_BR |
Rights | open access | pt_BR |
Title | Cutaneous manifestations in POEMS syndrome: case report and review | pt_BR |
Type | Article | pt_BR |
DOI | 10.1159/000381302 | |
Abstract | The authors report a case of sensorimotor polyneuropathy, diffuse cutaneous hyperpigmentation, skin sclerodermiform thickening and papular lesions in the infraclavicular and abdominal region. Besides weight loss, there were diabetes mellitus and hypothyroidism. The alterations were consistent with POEMS (Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal gammopathy and Skin changes) syndrome, which is a rare systemic disease with monoclonal proliferation of plasmacytes and slow progression. Cutaneous alterations are present in 68% of patients with diffuse cutaneous hyperpigmentation, plethora and acrocyanosis. Leukonychia, necrotizing vasculitis, hypertrichosis and cutaneous thickening of sclerodermiform type are also cited. The onset of multiple cutaneous angiomas in this syndrome has been observed in 24–44% of patients. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Neurology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Pathology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Affilliation | Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post-Graduation Course. Rio de Janeiro, RJ, Brazil. | pt_BR |
Subject | POEMS syndrome | pt_BR |
Subject | Plasmocytoma | pt_BR |
Subject | Polyneuropathy | pt_BR |
Subject | Endocrinopathy | pt_BR |
Subject | Monoclonal gammopathy | pt_BR |
Subject | Skin changes | pt_BR |
e-ISSN | 1662-6567 | |